|Full Name||methylcrotonoyl-CoA carboxylase 2 (beta)|
|Product Description||Rabbit Polyclonal antibody to MCCC2 (methylcrotonoyl-Coenzyme A carboxylase 2 (beta))|
|Background||This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. [provided by RefSeq]|
|Synonyms||MCCB antibody, MCCC2 antibody, 3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit antibody, 3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta antibody, biotin carboxylase antibody, MCCase subunit beta antibody, 3-methylcrotonyl-CoA carboxylase 2 antibody, "methylcrotonoyl-CoA carboxylase beta chain, mitochondrial antibody", methylcrotonoyl-Coenzyme A carboxylase 2 (beta) antibody, non-biotin containing subunit of 3-methylcrotonyl-CoA carboxylase antibody, methylcrotonoyl-CoA carboxylase 2 (beta) antibody|
|Cellular Localization||Mitochondrion matrix|
|Immunogen||Recombinant protein encompassing a sequence within the center region of human MCCC2. The exact sequence is proprietary.|
|Species Reactivity||Human, Mouse|
|Predicted Cross Reactivity species Predicted cross-reactivity:|
Predicted cross-reactivity is based on sequence homology, with greater than 80% immunogen sequence identity considered positive.
Please note that we are only able to guarantee products to work in applications and species in which they have been tested.
|Predict Reactivity Note||Rat (88%), Zebrafish (84%)|